Congenital cataracts

 

congenital-cataracts

What are congenital cataracts?

Congenital cataracts (or childhood cataracts) are cataracts that occur in children and are responsible for nearly 10% of all vision loss in children worldwide. They cause the lens of the eye to go cloudy, giving the eye a milky appearance and potentially causing visual impairment.

Older babies and toddlers can also get cataracts, referred to as paediatric cataracts.

Congenital Cataracts: types

Anterior polar cataracts

These are well-defined, although often considered too small to require surgical treatment. Located at the front of the eye's lens, they associate with inherited genes.

Posterior polar cataracts

Unlike the other types of congenital cataracts, these appear on the back of the eye’s lens.

Nuclear cataracts

The most common form of congenital cataracts, these appear in the middle of the eye.

Cerulean cataracts

Typically, this type of cataracts doesn't cause vision problems. Their small, pale blue dots easily distinguish them and are concentrated on the lens of the eye.

What causes congenital cataracts?

There is a range of reasons as to why children may be born with cataracts or develop them. In many cases, however, it is not possible to identify the exact cause.

Possible causes of congenital cataracts include the following:

Genetic conditions

Parents can sometimes pass on a faulty gene to their children which causes them to be born with cataracts.

Cataracts can also link to chromosome abnormalities and conditions such as Downs Syndrome which are caused by these abnormalities.

Infections during pregnancy

Various infections caught by the mother during pregnancy can also cause congenital cataracts. Viruses include rubella, toxoplasmosis, cytomegalovirus, chickenpox and herpes simplex virus.

A reaction to drugs

An example of this would be tetracycline antibiotics used to treat infections in pregnant women, which have proven to cause cataracts in newborn babies.

What are the signs and symptoms of Congenital Cataracts?

You'll be able to tell if a baby has congenital cataracts if:

  • Their pupil appears grey or white
  • You see a spot on the pupil
  • The pupil looks as though it has a film over it.

Can cataracts in children be prevented?

While it's not possible to prevent congenital cataracts that are inherited, listening to the advice given to you by your midwife during pregnancy can reduce the chances of your child having congenital cataracts.

Are congenital cataracts rare?

Congenital cataracts are rare, and according to the NHS, 3-4 in every 10,000 children are affected in the UK.

Can congenital cataracts get worse?

Congenital cataracts can get worse and can cause lazy eye or amblyopia. As a result, other eye problems affecting vision can arise such as nystagmus, strabismus and problems keeping a fixed gaze on objects.

Can congenital cataract cause blindness?

As well as causing lazy eye, cataracts, if not treated quickly, can cause irreversible damage such as blindness.

How are congenital cataracts treated?

In some cases, cataracts do not cause visual impairments; however, if the condition does begin to affect your child's sight, surgery may be recommended. Once a cataract is removed, it's unlikely to grow back.

If your doctor feels that the cataract will affect the development of your child's visual system, surgery, if the child is under the age of three months, is considered. However, if your child only has a cataract/cataracts in one eye, surgery may be required at a much earlier age.

Unilateral cataracts

Unilateral cataracts refer to having cataracts in one eye. In this case, the brain learns to switch off from the eye with a reduced vision. Instead, the brain relies on the eye without the cataract. When the brain does this, this prevents visual development in the eye with the cataract.

If the unilateral cataract is located in the centre of the lens and appears hefty, surgery to remove the cataract will take place early on to achieve the best visual outcome for the child. If this is not the case, using dilating eye drops is recommended in the healthy eye to force the child to use the eye, which is affected.

Nevertheless, even if the cataract is small, it can still cause amblyopia and therefore may still need cataract surgery.

Bilateral cataracts

Bilateral cataracts only affect a small area of a child's lenses. They can cause a limited visual system to develop. Some vision may worsen permanently. If the cataract is dense and affects your baby's vision, then an operation will be performed early on.

During surgery, the surgeon will make a small opening in the side of the cornea to remove the cloudy lens. The natural lens gets replaced with an artificial plastic lens called an intraocular lens or IOL, a lens implant that can last for life and does not usually need replacing. Alternatively, a contact lens or glasses, as opposed to a lens implant, may be suggested. Babies may find it difficult to wear glasses so doctors may recommend contact lenses for practicality.

What is the lifetime of a cataract lens?

A cataract lens typically lasts for a lifetime and is, therefore, a permanent fix.

Complications-Childhood cataracts

There is a low risk of severe complications with cataract surgery; however, some of the few risks which babies and children may experience include:

  • Posterior capsule opacification-this affects the artificial lens and can cause cloudy vision to come back
  • Glaucoma- where there is a build-up of pressure in the eye. If glaucoma is left untreated, it can permanently damage structures in the eye
  • Retinal detachment-when the retina detaches from the inner wall of the eye, affecting vision.
  • Infection-including rare bacterial infections such as endophthalmitis which can harm sight. If an infection develops, medication or additional surgery will be required to treat the infection
  • Cyst macular oedema-this can threaten vision and is where fluid builds up between the layers of the retina
  • Strabismus (squint)-where the eyes look in different direction
  • Pupil abnormalities-this doesn't usually affect vision but can include changes to the pupil, for example, it may become more oval-shaped

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